Midostaurin

Midostaurin, sold under the brand name Rydapt by Novartis, is a multi-targeted protein kinase inhibitor that has been investigated for the treatment of acute myeloid leukemia (AML), myelodysplastic syndrome (MDS) and advanced systemic mastocytosis.[3] Midostaurin was found to be active against oncogenic CD135 (FMS-like tyrosine kinase 3 receptor, FLT3), in preclinical studies.After successful Phase II clinical trials, midostaurin was found to prolong survival of FLT3-mutated AML patients when combined with conventional induction and consolidation therapies in a randomized Phase III clinical trial.[5] On 28 April 2017, midostaurin was approved by the FDA for the treatment of adult patients with newly diagnosed AML who are positive for oncogenic FLT3, in combination with chemotherapy.[7] Common side effects include immune system related problems (fever, febrile neutropenia), blood clotting problems (bruising, nosebleed), and unspecific symptoms such as diarrhea, nausea and headache.
Drugs.comRoutes ofadministrationBy mouthATC codeL01EX10Legal status ℞-only℞-onlyIUPAC nameCAS NumberIUPHAR/BPSDrugBankChemSpiderChEMBLCompTox DashboardFormulaMolar massSMILESNovartisprotein kinase inhibitoracute myeloid leukemiamyelodysplastic syndromesystemic mastocytosisstaurosporinealkaloidStreptomycesFood and Drug Administrationfirst-in-class medicationrefractoryclinical trialsinductionmastocytosiscutaneousopen-label studymast cell leukemiafebrile neutropeniablood clottingnauseaUpper respiratory tract infectionsHealth CanadaTargeted cancer therapyantineoplastic agentsmonoclonal antibodiesReceptor tyrosine kinaseHER1/EGFRCetuximabPanitumumabHER2/neuPertuzumabTrastuzumab+hyaluronidaseTrastuzumab emtansineTrastuzumab deruxtecanZanidatamabCatumaxomabEdrecolomabVEGF-ABevacizumabLeukemialymphomalymphoidGlofitamabElranatamabMosunetuzumabIbritumomabObinutuzumabOfatumumabRituximabTositumomabBrentuximabAlemtuzumabmyeloidGemtuzumab ozogamicinAmivantamabAtezolizumabAvelumabAxatilimabBelantamab mafodotinBermekimabBlinatumomabCemiplimabCosibelimabDaratumumabDinutuximab betaDostarlimabDurvalumabElotuzumabEnfortumab vedotinEpcoritamabInotuzumab ozogamicinIpilimumabIsatuximabLoncastuximab tesirineMirvetuximab soravtansineMogamulizumabMoxetumomab pasudotoxNaxitamabNecitumumabNivolumab+relatlimabOlaratumabOportuzumab monatoxPembrolizumabPolatuzumab vedotinRamucirumabRetifanlimabSacituzumab govitecanSerplulimabSugemalimabTafasitamabTalquetamabTarlatamabTeclistamabTislelizumabTisotumab vedotinToripalimabTremelimumabZenocutuzumabZolbetuximabTyrosine kinase inhibitorsAfatinibAumolertinibBrigatinibDacomitinibErlotinibGefitinibIcotinibLazertinibMobocertinibOlmutinibOsimertinibRociletinibVandetanibLapatinibNeratinibTucatinibDabrafenibEncorafenibTovorafenibVemurafenibRTK class IIIAvapritinibAxitinibMasitinibPazopanibRipretinibSorafenibSunitinibToceranibLestaurtinibGilteritinibCediranibFruquintinibLenvatinibNintedanibRegorafenibSemaxanibTivozanibAlectinibCeritinibCrizotinibEnsartinibLorlatinibEntrectinibFutibatinibInfigratinibLarotrectinibPemigatinibPralsetinibRepotrectinibSelpercatinibCabozantinibCapmatinibNon-receptorbcr-ablAsciminibBosutinibDasatinibImatinibNilotinibPonatinibRadotinibJanus kinaseBaricitinibFedratinibFilgotinibMomelotinibPacritinibRuxolitinibBinimetinibCobimetinibSelumetinibTrametinibBruton'sAcalabrutinibIbrutinibOrelabrutinibPirtobrutinibZanubrutinibfusion proteinAfliberceptproapoptoticprohibitinAdipotideexotoxinDenileukin diftitoxmTOR inhibitorsEverolimusRidaforolimusSirolimusTemsirolimushedgehogGlasdegibSonidegibVismodegibCDK inhibitorsAbemaciclibDalpiciclibPalbociclibRibociclibTrilaciclibAdagrasibSotorasibPi3K inhibitorsAlpelisibCopanlisibDuvelisibIdelalisibInavolisibParsaclisibRevumenibFibroblast growth factor receptorErdafitinibOdronextamabPexidartinibQuizartinibTebentafuspTepotinibTunlametinibVenetoclaxCytokine receptormodulatorsChemokineErythropoietinDarbepoetin alfaEpoetin alfaEpoetin betaEpoetin thetaEpoetin zetaErythropoietin (EPO)Methoxy polyethylene glycol-epoetin beta (CERA/Mircera)PeginesatideG-CSF (CSF3)FilgrastimGranulocyte colony-stimulating factorLenograstimLipegfilgrastimPegfilgrastimGM-CSF (CSF2)Granulocyte macrophage colony-stimulating factorMolgramostimSargramostimMavrilimumabNamilumabOtilimabM-CSF (CSF1)Interleukin-34Macrophage colony-stimulating factorSCF (c-Kit)ThrombopoietinEltrombopagPromegapoietinRomiplostimThrombopoietin (THPO, MGDF)InterferonIFNAR (α/β, I)AlbinterferonInterferon alpha (interferon alfa, IFN-α)Interferon alfaIFNA10IFNA13IFNA14IFNA16IFNA17IFNA21Interferon alfa 2aInterferon alfa 2bInterferon alfacon-1Interferon alpha-n3Interferon beta (IFN-β)Interferon beta 1aInterferon beta 1bInterferon kappa (IFN-ε/κ/τ/ζ, IFNK)Interferon omega (IFN-ω, IFNW1)Peginterferon alfa-2aPeginterferon alfa-2bAnifrolumabFaralimomabRontalizumabSifalimumabIFNGR (γ, II)Interferon gamma (IFN-γ)Interferon gamma 1bEmapalumabFontolizumabIFNLR (λ, III)InterleukininhibitorsAbrocitinibDeuruxolitinibOclacitinibPeficitinibTofacitinib (tasocitinib)UpadacitinibAtiprimodCHZ868Cucurbitacin I (elatericin B, JSI-124)CYT387Decernotinib (VX-509)RitlecitinibDeucravacitinibCardiotrophin 1 (CT-1)FMS-like tyrosine kinase 3 ligand (FLT3L)Leukemia/leukocyte inhibitory factor (LIF)Oncostatin M (OSM)Thymic stromal lymphopoietin (TSLP)