Mucous membrane pemphigoid

When the condition is active, the basement membrane is dissolved by the antibodies produced, and areas of skin lift away at the base, causing hard blisters which scar if they burst.In other words, this is a desquamating/blistering disease in which the epithelium "unzips" from the underlying connective tissue, allowing fluid to gather that subsequently manifest as bullae, or blisters.Oral candidiasis may develop with long term topical steroid use, and sometimes antimycotics such as miconazole gel or chlorhexidine mouthwash are used to prevent this.Many other drugs have been used to treat mucous membrane pemphoid, including azathioprine, cyclophosphamide, methotrexate, thalidomide, mycophenolate mofetil, leflunomide, sulphasalazine, sulphapuridine, sulphamethoxypiridazine, tetracyclines (e.g. minocycline, doxycycline) and nicotinamide.Sometimes surgical procedures are required to repair scars, prevent complications such as blindness, upper airway stenosis or esophageal stricture.
SpecialtyDermatologyautoimmuneblisteringlesionsmucous membranespemphigoid diseasesoral mucosadesquamative gingivitiscorneaepidermolysis bullosa acquisitaNikolsky's signpemphigusbullous pemphigoidbasement membraneepitheliumbullaeantibodieslamina lucidahemidesmosomeNikolsky signsystemic drugsTopicaloral hygienedental scalingcorticosteroidfluocinonideclobetasol propionatetriamcinolone acetonideOral candidiasisantimycoticsmiconazolechlorhexidineciclosporinDapsoneprednisoneprednisoloneazathioprinecyclophosphamidemethotrexatethalidomidemycophenolate mofetilleflunomidesulphasalazinetetracyclinesminocyclinedoxycyclinenicotinamidePlasmapheresisGestational pemphigoidList of cutaneous conditionsList of target antigens in pemphigoidList of immunofluorescence findings for autoimmune bullous conditionsDiseasesDBPatient UKEpidermalCallusSeborrheic keratosisAcrochordonMolluscum contagiosumActinic keratosisSquamous-cell carcinomaBasal-cell carcinomaMerkel-cell carcinomaNevus sebaceousTrichoepitheliomaFrecklesLentigoMelasmaMelanomaPostinflammatory hyperpigmentationDermalEpidermal inclusion cystHemangiomaDermatofibroma (benign fibrous histiocytoma)KeloidLipomaNeurofibromaXanthomaKaposi's sarcomaInfantile digital fibromatosisGranular cell tumorLeiomyomaLymphangioma circumscriptumMyxoid cystRashesContact dermatitisAtopic dermatitisSeborrheic dermatitisStasis dermatitisLichen simplex chronicusDarier's diseaseGlucagonoma syndromeLangerhans cell histiocytosisLichen sclerosusPemphigus foliaceusWiskott–Aldrich syndromeZinc deficiencyScalingPsoriasisCorporisCrurisManuumFacieiPityriasis roseaSecondary syphilisMycosis fungoidesSystemic lupus erythematosusPityriasis rubra pilarisParapsoriasisIchthyosisHerpes simplexHerpes zosterVaricellaBullous impetigoAcute contact dermatitisPemphigus vulgarisDermatitis herpetiformisPorphyria cutanea tardaEpidermolysis bullosa simplexPapularScabiesInsect bite reactionsLichen planusMiliariaKeratosis pilarisLichen spinulosusTransient acantholytic dermatosisLichen nitidusPityriasis lichenoides et varioliformis acutaPustularAcne vulgarisRosaceaFolliculitisImpetigoCandidiasisGonococcemiaDermatophyteCoccidioidomycosisSubcorneal pustular dermatosisTinea versicolorVitiligoPityriasis albaTuberous sclerosisIdiopathic guttate hypomelanosisLeprosyHypopigmented mycosis fungoidesErythemaDrug eruptionsViral exanthemsToxic erythemaCellulitisAbscessErythema nodosumCarcinoid syndromeFixed drug eruptionUrticariaMultiformeMigransGyratum repensAnnulare centrifugumAb igneThrombocytopenic purpuraActinic/solar purpuraDisseminated intravascular coagulationVasculitisSclerodermamorpheaGranuloma annulareLichen sclerosis et atrophicusNecrobiosis lipoidicaUlcersTelogen effluviumAndrogenic alopeciaAlopecia areataTinea capitisLoose anagen syndromeLichen planopilarisFolliculitis decalvansAcne keloidalis nuchaeOnychomycosisParonychiaIngrown nailMucous membraneAphthous stomatitisLeukoplakiaCicatricial pemphigoidHerpesvirusCoxsackievirusSyphilisSystemic histoplasmosisVesiculobullous diseaseAcantholysisepidermisPemphigus vegetansof Hallopeauof NeumannPemphigus erythematosusEndemic pemphigusParaneoplastic pemphigusIgA pemphigusSubcorneal pustularIntraepidermal neutrophilicPemphigoiddermisLocalisedPemphigoid nodularisLinear IgA bullous dermatosisChildhoodbullousBullous lupus erythematosusPUVA-induced acrobullous dermatosis