Lymphoproliferative disorders

Lymphoproliferative disorders (LPDs) refer to a specific class of diagnoses, comprising a group of several conditions, in which lymphocytes are produced in excessive quantities.[citation needed] Some children with autoimmune lymphoproliferative disorders are heterozygous for a mutation in the gene that codes for the Fas receptor, which is located on the long arm of chromosome 10 at position 24.1, denoted 10q24.1.[2] Boys with X-linked immunodeficiency syndrome are at a higher risk of mortality associated with Epstein–Barr virus infections, and are predisposed to develop a lymphoproliferative disorder or lymphoma.[citation needed] Children with common variable immunodeficiency (CVID) are also at a higher risk of developing a lymphoproliferative disorder.In children, the most common is believed to be congenital HIV infection because it is highly associated with acquired immunodeficiency, which often leads to lymphoproliferative disorders.
SpecialtyHematologyoncologylymphocytesimmune systemimmunoproliferative disordersnomenclaturesubclasshypergammaglobulinemiaparaproteinemiasFollicular lymphomaChronic lymphocytic leukemiaAcute lymphoblastic leukemiaHairy cell leukemiaHemophagocytic lymphohistiocytosisB-cell lymphomasT-cell lymphomasMultiple myelomaWaldenström's macroglobulinemiaWiskott–Aldrich syndromeLangerhans cell histiocytosisLymphocyte-variant hypereosinophiliaPityriasis lichenoidesPost-transplant lymphoproliferative disorderAutoimmune lymphoproliferative syndromeLymphoid interstitial pneumoniaEpstein–Barr virus-associated lymphoproliferative diseasesCastleman diseaseX-linked lymphoproliferative diseasePrimary cutaneous acral CD8 positive T cell lymphoproliferative disordermonoclonallymphocytosisB cellsT cellspluripotenthematopoietic stem cellsbone marrowimmunodeficiencygene mutationsiatrogenicX chromosomenatural killer cellFas receptorchromosome 10apoptosisEpstein–Barr viruscommon variable immunodeficiencysevere combined immunodeficiencyChédiak–Higashi syndromeataxia–telangiectasiaheterozygotesViral infectionorgan transplantationimmunosuppressantsirolimustacrolimusciclosporinEpstein-Barr virusEpstein-Barr virus-associated lymphoproliferative diseasesEvans syndromeLeukaemiaLymphomaMyelomaMyeloproliferative diseaseeMedicineLeukaemiaslymphomasleukemiaPrecursor B acute lymphoblastic leukemia/lymphomanaive B cellCLL/SLLmantle zoneMantle cellProlymphocyticCD11c+germinal centerfollicular B cellFollicularBurkitt'sGCB DLBCLPrimary cutaneous follicle center lymphomaPrimary mediastinal B-cell lymphomamarginal zonemarginal zone B-cellSplenic marginal zoneNodal marginal zonePrimary cutaneous marginal zone lymphomaClassic Hodgkin lymphomaNodular sclerosisNodular lymphocyte predominant Hodgkin lymphomaPrimary effusionLymphomatoid granulomatosisBurkitt's lymphomaSplenic marginal zone lymphomaAIDS-related lymphomaHelicobacter pyloriMALT lymphomaCutaneousDiffuse large B-cell lymphomaIntravascular large B-cell lymphomaPrimary cutaneous immunocytomaPlasmacytomaPlasmacytosisT cellPrecursor T acute lymphoblastic leukemia/lymphomaprolymphocyteAnaplastic large-cell lymphomaLymphomatoid papulosis type AMF+variantsMycosis fungoidesPagetoid reticulosisGranulomatous slack skinSézary diseaseAdult T-cell leukemia/lymphomaNon-mycosis fungoides CD30− cutaneous large T-cell lymphomaPleomorphic T-cell lymphomaLymphomatoid papulosis type BCD30+ cutaneous T-cell lymphomaSecondary cutaneous CD30+ large-cell lymphomaperipheralHepatosplenicAngioimmunoblasticEnteropathy-associated T-cell lymphomaPeripheral T-cell lymphoma not otherwise specifiedLennert lymphomaSubcutaneous T-cell lymphomaHTLV-1Aggressive NK-cell leukemiaBlastic NK cell lymphomaExtranodal NK-T-cell lymphomaAngiocentric lymphomaLarge granular lymphocytic leukemiaAcute biphenotypic leukaemiaLeukemoid reactionDiffuse infiltrative lymphocytosis syndromeCutaneous lymphoid hyperplasiawith bandlike and perivascular patternswith nodular patternJessner lymphocytic infiltrate of the skinHematological malignancyLeukemia cutisLymphoid leukemias