Desmoplastic fibroma

In medicine, a desmoplastic fibroma is a low-grade malignant, locally aggressive, fibrous and rare tumor of the bone, affecting children and young adults, potentially resulting in cortical bone destruction.[2] Although it does not tend to metastatize, it has a high local recurrence and infiltrative growth.[3] Treatment consists in wide local excision to prevent otherwise frequent recurrences.[4] The role of radiotherapy and chemotherapy in this tumor still is unclear.[6] A famous occurrence of this particular form of the disease involved Italo-Australian Riccardo Torresan in 2011, with 18 cm of femur needing to be removed with the now widely recognized method of "aggressive curettage" being employed.
Specialtymedicinelow-grademalignantcortical bonefibroblastic and myofibroblastic tumorsmetastatizeradiotherapychemotherapyosteosarcomaDesmoplasiaDiseasesDBSNOMED CTConnectivesoft tissuetumorssarcomasSoft-tissue sarcomaDesmoplastic small-round-cell tumorSkin sarcomaConnective tissue neoplasmFibromatousFibromafibrosarcomaDermatofibrosarcoma protuberansfibromatosisAggressive fibromatosisAggressive infantile fibromatosisAponeurotic fibromaCollagenous fibromaDiffuse infantile fibromatosisFibroma of tendon sheathFibromatosis colliInfantile digital fibromatosisJuvenile hyaline fibromatosisPlantar fibromatosisPleomorphic fibromaOral submucous fibrosisPachydermodactylyHistiocytomahistiocytic sarcomaBenign fibrous histiocytomaMalignant fibrous histiocytomaAtypical fibroxanthomaSolitary fibrous tumorMyxomatousMyxomamyxosarcomaCutaneous myxomaSuperficial acral fibromyxomaAngiomyxomaOssifying fibromyxoid tumourFibroepithelialBrenner tumourFibroadenomaPhyllodes tumorSynovialSynovial sarcomaClear-cell sarcomaLipomatousLipomaliposarcomaMyelolipomaMyxoid liposarcomaPEComaAngiomyolipomaChondroid lipomaIntradermal spindle cell lipomaPleomorphic lipomaLipoblastomatosisSpindle cell lipomaHibernomaMyomatousmyosarcomaSmooth muscleLeiomyomaleiomyosarcomaSkeletal muscleRhabdomyomarhabdomyosarcomaEmbryonal rhabdomyosarcomaSarcoma botryoidesAlveolar rhabdomyosarcomaCutaneousAngioleiomyomaAngiolipoleiomyomaGenital leiomyomaMultiple cutaneous and uterine leiomyomatosis syndromeMultiple cutaneous leiomyomaNeural fibrolipomaSolitary cutaneous leiomyomaComplex mixed and stromalAdenomyomaPleomorphic adenomaMixed Müllerian tumorMesoblastic nephromaWilms' tumorMalignant rhabdoid tumourClear-cell sarcoma of the kidneyHepatoblastomaPancreatoblastomaCarcinosarcomaMesothelialMesotheliomaAdenomatoid tumoroncology